Spectrum of Spinal Dysraphism in Pediatric Patients in a Tertiary Care Hospital

  • Musawer Khan Neurosurgeon
  • Arif Hussain Department of Neurosurgery, MTI Lady Reading Hospital
  • Huma Gul District Headquarters Hospital, Mardan
  • Ambreen Syed Hayatabad Medical Complex, Peshawar
Keywords: Spinal Dysraphism, Endoscopic third Ventriculostomy, Ventriculoperitoneal, Myelomeningocele, Tethered Cord Syndrome

Abstract

Objectives:  To report the spectrum of spinal dysraphism presenting in pediatric patients admitted to the Department of Neurosurgery Lady reading hospital Peshawar.

Material & Methods:  A descriptive case series was conducted and total of 89 patients (age between 2 months to 12 years) were included who underwent the surgical treatment. All patients were examined for clinical and radiological diagnosis of spinal dysraphism.

Results:  The average age at treatment was 23 ± 39.77 months. The most recurring (52.8%) presenting symptom was the swelling on the back followed by lower limb weakness. Meningocele was reported in 11.2%, myelomeningocele in 47.2%, myelomeningocele & hydrocephalus in 12.4%, tethered cord syndrome in 25.8%, and diastematomyelia 3.4% of patients. Excision combined with the repair was done in 58.4%, release & repair done in 29.2% and endoscopic third ventriculostomy/ventriculoperitoneal shunts with the repair were done in 12.4% patients. Cerebrospinal fluid leak was reported in 3.7%, wound infection in 4.5% and mortality was reported in 3.4% patients.

Conclusion:  Overall, a good outcome was reported in the majority of our patients. Surgical procedures like myelomeningocele’s excision & repair, tethered cord’s release & repair, and ETV/VP shunt in patients with hydrocephalus can lead to satisfactory clinical outcomes.

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Published
2021-06-14
Section
Original Articles