Primary Soft Tissue Orbital Ewing’s Sarcoma Causing Unilateral Visual Loss: A Case Report
Abstract
A case of primary Ewing's sarcoma of right orbit causing unilateral visual loss in a 3 year old female child is reported. The child presented with 1 year history of painless unilateral proptosis and loss of vision. Loss of vision due to primary Ewing's sarcoma in orbit is extremely rare and it should be considered as one of the differential diagnoses while dealing the patient with these sorts of clinical presentation.
References
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9. Woodruff G, Thorner, Skarf B. Primary Ewing’s sarco-ma of the orbit presenting with visual loss. British Jour-nal of Ophthalmology, 1988; 72: 786-792. 10. Dutton JJ, Rose JG, Jr, DeBacker CM, Gayre G. Orbital Ewing’s sarcoma of the orbit. Ophthal Plast Reconstr Surg., 2000; 16: 292–300. 11. Sabharwal K, Chouhan A, Jain S. CT evaluation of pro-ptosis. Indian J Radiol Imaging, 2006; 16: 683–8. 12. Margo CE, Mulla ZD. Malignant tumors of the orbit. Analysis of the Florida Cancer Registry. Ophthalmo-logy, 1998; 105: 185–90. 13. Reese AB. Expanding lesions of the orbit. Trans Oph-thalmol Soc U K, 1971; 91: 85–104. 14. Shields JA, Bakewell B, Augsburger JJ, Flanagan JC. Classification and incidence of space – occupying les-ions of the orbit. A survey of 645 biopsies. Arch Oph-thalmol., 1984; 102: 1606–11. 15. Basit Ali Syed. Primary intracranial Ewing’s sarcoma of calvarium presenting as acute neurosurgical emer-gency. Case report and literature Review. Pan Arab J Neurosurg., 1999; 3: 1. 16. Bhatoe HS, Deshpande GU. Primary cranial Ewing's sarcoma. Br J Neurosurg., 1998; 12: 165–71. 17. Alvarez – Berdecia A, Schut L, Bruce DA. Localized primary intracranial Ewing’s sarcoma of the orbital roof. Case report. J Neurosurg., 1979; 50: 811–3. 18. Gupta N, Bansal D, Saxena AK, Srinivasan R, Mar-waha RK. Primary orbital Ewing's sarcoma presenting with unilateral proptosis. Cytopathology, 2008; 19: 124–6. 19. Perlman EJ, Dickman PS, Askin FB, Grier HE, Miser JS, Link MP. Ewing’s sarcoma – routine diagnostic uti-lization of MIC2 analysis: A Pediatric Oncology Group/ Children’s Cancer Group Intergroup Study. Hum Pa-thol., 1994; 25: 304–7. 20. Roessner A, Jürgens H. Round cell tumours of bone. Pathol Res Pract., 1993; 189: 111–36. 21. Lam DS, Li CK, Cheng LL, Teo JG, Chik KW, Kwan WH, et al. Primary orbital Ewing’s sarcoma: Report of
2. Coley BL, Higinbotham NL, Bowden L. Endothelioma of bone (Ewing’s sarcoma). Ann Surg, 1948; 128: 533-60.
3. Jaffe R, Santamaria M, Yunis EJ, et al. The neuroecto-dermal tumour of bone. Am J Surg PathoI, 1984; 8: 885-98.
4. Arndt CA, Crist WM. Common musculoskeletal tumors of childhood and adolescence. N Engl J Med., 1999; 29: 341–52.
5. Kennedy JG, Eustace S, Caulfield R, Fennelly DJ, Hur-son B, O’Rourke KS. Extraskeletal Ewing's sarcoma: A case report and review of the literature. Spine, 2000; 25: 1996–9.
6. Wilkins RM, Pritchard DJ, Burgert EO Jr, Unni KK. Ewing’s sarcoma of bone. Experience with 140 pati-ents. Cancer, 1986; 58: 2551-5. 7. Ewing J. Diffuse endothelioma of bone. Proc N Y Pa-thol Soc., 1921; 21: 17-24. 8. Kano T, Sasaki A, Tomizawa S, Shibasaki T, Tamura M, Ohye C. Primary Ewing’s sarcoma of the orbit: case report. Brain Tumor Pathol., 2009; 26 (2): 95-100.
9. Woodruff G, Thorner, Skarf B. Primary Ewing’s sarco-ma of the orbit presenting with visual loss. British Jour-nal of Ophthalmology, 1988; 72: 786-792. 10. Dutton JJ, Rose JG, Jr, DeBacker CM, Gayre G. Orbital Ewing’s sarcoma of the orbit. Ophthal Plast Reconstr Surg., 2000; 16: 292–300. 11. Sabharwal K, Chouhan A, Jain S. CT evaluation of pro-ptosis. Indian J Radiol Imaging, 2006; 16: 683–8. 12. Margo CE, Mulla ZD. Malignant tumors of the orbit. Analysis of the Florida Cancer Registry. Ophthalmo-logy, 1998; 105: 185–90. 13. Reese AB. Expanding lesions of the orbit. Trans Oph-thalmol Soc U K, 1971; 91: 85–104. 14. Shields JA, Bakewell B, Augsburger JJ, Flanagan JC. Classification and incidence of space – occupying les-ions of the orbit. A survey of 645 biopsies. Arch Oph-thalmol., 1984; 102: 1606–11. 15. Basit Ali Syed. Primary intracranial Ewing’s sarcoma of calvarium presenting as acute neurosurgical emer-gency. Case report and literature Review. Pan Arab J Neurosurg., 1999; 3: 1. 16. Bhatoe HS, Deshpande GU. Primary cranial Ewing's sarcoma. Br J Neurosurg., 1998; 12: 165–71. 17. Alvarez – Berdecia A, Schut L, Bruce DA. Localized primary intracranial Ewing’s sarcoma of the orbital roof. Case report. J Neurosurg., 1979; 50: 811–3. 18. Gupta N, Bansal D, Saxena AK, Srinivasan R, Mar-waha RK. Primary orbital Ewing's sarcoma presenting with unilateral proptosis. Cytopathology, 2008; 19: 124–6. 19. Perlman EJ, Dickman PS, Askin FB, Grier HE, Miser JS, Link MP. Ewing’s sarcoma – routine diagnostic uti-lization of MIC2 analysis: A Pediatric Oncology Group/ Children’s Cancer Group Intergroup Study. Hum Pa-thol., 1994; 25: 304–7. 20. Roessner A, Jürgens H. Round cell tumours of bone. Pathol Res Pract., 1993; 189: 111–36. 21. Lam DS, Li CK, Cheng LL, Teo JG, Chik KW, Kwan WH, et al. Primary orbital Ewing’s sarcoma: Report of
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2018-09-30
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