Recurrent Occipital Dermatofibrosarcoma Protuberans: Multidisciplinary Management of a Rare Case

Multidisciplinary management of a rare case

  • Mubashir Malik Department of Neurosurgery, PINS, Lahore.
  • Zubair Ahmed Khan Department of Neurosurgery, Punjab Institute of Neurosciences, Lahore – Pakistan
  • Rabia Saleem Department of Neurosurgery, Punjab Institute of Neurosciences, Lahore – Pakistan
  • Shahzad Safdar Department of Neurosurgery, Punjab Institute of Neurosciences, Lahore – Pakistan
  • Touqeer Ahmed Department of Neurosurgery, Punjab Institute of Neurosciences (PINS), Lahore, Pakistan
Keywords: Dermatofibrosarcoma (DFSP), occipital bone, multidisciplinary, wide local excision.


Dermatofibrosarcoma protuberance is a skin tumor arising from dermis, slow growing in nature and locally invasive. Most commonly present on extremities and rarely on head and neck region. We are presenting a case of 24 years old male with huge recurrent DFSP lesion in occipital region. We did wide local excision with tumor free skin margins of 2.5cm followed by excision of involved occipital bone and wound coverage with carotid artery flap. DFSP is challenging skin tumor with high recurrence rate and should be managed by multidisciplinary approach.


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Case Reports