Dysembryoplastic Neuroepithelial Tumour (DNET): A Rare Brain Pathology Presenting with Intractable Seizures

Authors

  • Yaser-ud-Din Hoti All at Department of Neurosurgery, PGMI / AMC and Lahore General Hospital, Lahore
  • Khurram Ishaque Department of Neurosurgery, PGMI / AMC and Lahore General Hospital, Lahore
  • Amir Aziz Department of Neurosurgery, PGMI / AMC and Lahore General Hospital, Lahore
  • Bashir Ahmed Department of Neurosurgery, PGMI / AMC and Lahore General Hospital, Lahore
  • Tariq Salah-ud-Din Department of Neurosurgery, PGMI / AMC and Lahore General Hospital, Lahore

Keywords:

Dysembryoplastic neuroepithelial tumour (DNET),, glioneural, malignant, brain tumors.

Abstract

Dysembryoplastic neuroepithelial tumour (DNET) is a benign glioneuronal tumour often related with intractable localization – related seizures in both in paediatric age group as well as young adults. However, a small number appear to have the potential for malignant transformation. Total surgical removal without any adjuvant therapy is the gold standard treatment. We report a case in which DNET appeared in a 13 year old male. Cranial CT scan showed a discoid lesion with peripheral enhancement in right parietal lobe. Micro-decompression of the tumour was done. On histopathology, the tumour revealed features of WHO grade I dysembryoplastic neuroepithelial tumour.

References

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Published

2014-12-30

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Original Articles