Pattern of Presentation of Spinal Dysraphism
Keywords:
spinal dysraphism, spina bifida apertaAbstract
Objective: To assess the pattern of presentation of spinal dysraphism and compare with already available data on the subject.
Design: Prospective study.
Material and Method: This prospective study was done in the department of Neurosurgery, King Edward Medi-cal University (KEMU) Lahore, Pakistan from January 2008 to December 2009. Cases of spinal dysraphism admitted and managed in the department during this period were included in the study.
Results: Total patients admitted with spinal dysraphism during this period were 56. Of them, spina bifida aperta were 42 (75%) and occulta were 14 (25%). Age range of patients of spinal dysraphism was from 1 day to 27 years. Male to female ratio was 1.5 : 1. All the patients of spina bifida aperta had myelomeningocele i.e. 42 (75%). Of them maximum patients had myelomeningocele at lumbosacral region i.e. 18 (42%) followed by lumbar area i.e. 11 (26%). No patients had cervical spina bifida aperta. Hydrocephalus was present in 32 (76%) patient. Of 56 cases of spinal dysraphism, 14 (25%) had spina bifida occulta. Among spina bifida occulta, lipo-myelomeningocele and congenital dermal sinus were 5 (9%) each while 4 (7%) patients had meningocele. All patients had x-ray spine of the affected region. All patients of spina bifida occulta had MRI brain and whole spine.
Conclusion: All patients of spina bifida aperta presented with myelomeningocele, commonest at lumbosacral area. Age at presentation was relatively late. Of spina bifida occulta, Lipomyelomeningocele and congenital der-mal sinus were unusually equal. Meningocele was relative less.
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