Recurrent Cervical Neurofibrosarcoma: A Rare Case of Malignant Peripheral Nerve Sheath Tumor of Head and Neck Region

  • Mubashir Malik Department of Neurosurgery, PINS, Lahore.
  • Zubair Ahmed Khan
  • Umer Farooq
  • Shehzad Safdar
  • aSAD ur Rehman
  • Noman Saleem
Keywords: Neurofibrosarcoma, Neurofibromatosis type 1

Abstract

Neurofibrosarcoma is a malignant peripheral nerve sheath tumor (MPNST). The cervical location of the neurofibrosarcoma is very rare and is less than 1% in the literature. MPNSTs are often associated with neurofibromatosis type 1 (NF1).  We are presenting a case report of 31 years old female, with huge recurrent cervical neurofibrosarcoma on the right side of the neck.  To date, surgical excision followed by chemotherapy and radiotherapy is the treatment of choice which requires a multidisciplinary approach. We excised the above-mentioned cervical neurofibrosarcoma in a piecemeal fashion and discharged the patient on follow-up with the oncology department.

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Published
2022-01-05
Section
Case Reports